An anomalous origin of the right pulmonary artery is a rare phenomenon in neonates with transposition of the great arteries. We report a case of dextro-transposition of the great arteries with an anomalous right pulmonary artery originating from the innominate artery, diagnosed by cardiac CT angiography and the cinematic rendering technique. Although surgical correction was possible, it was deferred due to complex anatomy and parental preference. This case highlights the diagnostic value and role of advanced imaging in complex congenital heart disease.

Takotsubo cardiomyopathy, also known as stress cardiomyopathy or broken heart syndrome, is named for echocardiographic features that look like the “tako-tsubo” (octopus trap). While classically associated with older women after experiencing significant emotional distress, it can also occur in paediatrics. Our patient is an 11-year-old male with a complex medical history who developed Takotsubo cardiomyopathy after cardiac arrest during anaesthesia induction. He was successfully resuscitated, but this case highlights an example of an unusual drug interaction and the first of its description in paediatrics.

Thoracotomy-assisted arterial duct stenting is a palliative option for patent ductus arteriosus-dependent systemic circulation, typically reserved for infants at high risk for open-heart surgery, such as those with genetic syndromes or very low birth weight. We report the first documented case of thoracotomy-assisted arterial duct stenting in a patient with Kleefstra syndrome, resulting in systemic stabilisation and long-term survival.

Venous thrombosis in the Fontan circulation can be a devastating complication, and its management has traditionally been surgical. Here, we present two cases of extensive Fontan thrombosis that have both been successfully medically managed, with survival beyond two years.

A patient with Kabuki syndrome and a parachute mitral valve was referred for mitral stenosis. Echocardiography indicated right ventricular dilatation and a suspected vertical ascending vein. Cardiac CT confirmed dual drainage of the left upper pulmonary vein and hemiazygos vein continuity. Despite echocardiographic limitations, surgery was performed. This rare case is reported due to its unique anatomical variation.

Sternal cleft is a rare congenital condition associated with unprotected viscera and respiratory failure. We present a case of a sternal cleft, absent right clavicle, and congenital diaphragmatic paresis in a neonate. The sternum was closed primarily, and the patient was taken back for plication of the diaphragm. At 3 years follow-up, the patient is free from complications.

Total anomalous pulmonary venous drainage associated with hypoplastic aortic arch represents an exceptionally rare and intricate congenital cardiac anomaly. We report the case of a 13-day-old late preterm neonate presenting with infracardiac total anomalous pulmonary venous drainage, severe pulmonary hypertension, and a hypoplastic aortic arch. The patient underwent single-stage surgical correction involving rerouting of the pulmonary venous confluence to the left atrium and aortic arch reconstruction using autologous pericardial patch under cardiopulmonary bypass with selective cerebral perfusion. Postoperative recovery was favourable, marked by successful extubation, resolution of pulmonary hypertension, and absence of residual anatomical obstruction. This case highlights the feasibility and effectiveness of early, comprehensive surgical repair and the necessity of coordinated multidisciplinary perioperative care. Long-term follow-up remains vital for monitoring functional outcomes and detecting late complications.

Ductus arteriosus aneurysm typically resolves spontaneously; surgical resection is required when it compresses surrounding structures and causes symptoms. In our neonatal case, the ductus arteriosus gradually regressed, but the left pulmonary artery stenosis persisted; therefore, balloon dilation was performed to address the ongoing imbalance in bilateral pulmonary perfusion. This case underscores the potential for non-surgical management of ductus arteriosus aneurysms.

We report a 7-year-old boy with tetralogy of Fallot who developed a right ventricular pseudoaneurysm one year after right ventricular outflow tract reconstruction with a 17 mm pulmonary homograft. Urgent reoperation revealed proximal homograft dehiscence. Repair was performed using an Invengenx® pericardial patch. This rare complication highlights the importance of long-term surveillance following homograft implantation in congenital heart surgery.

Giant left atrium is extremely rare in the paediatric population, especially in asymptomatic cases. We report a 5-year-old child with a giant left atrium due to “non-rheumatic” mitral valve regurgitation that presented as a stroke secondary to atrial tachycardia. This case is noteworthy for the unusual “silent” manifestation of a giant left atrium.

Tricuspid valve repair in paediatric infective endocarditis using a right axillary thoracotomy approach has never been reported. This report describes the minimally invasive treatment of infective endocarditis using this approach in a previously healthy paediatric patient. The patient underwent successful tricuspid valve repair and was discharged with an outpatient antibiotic regimen. He remains well seven months postoperatively.

An adolescent girl with a long-standing history of pulmonary arterial hypertension experienced severe clinical decompensation after starting to use e-cigarettes. A combination of e-cigarette cessation, atrial septostomy, increasing treprostinil, and initiation of sotatercept led to clinical improvement. Her new baseline was improved over her pre-e-cigarette baseline.

We report the first case in Vietnam of transcatheter pulmonary valve-in-valve implantation using the self-expanding Pulsta valve in a young adult with repaired Tetralogy of Fallot. This case demonstrates the feasibility, safety, and early effectiveness of self-expanding valves in complex right ventricular outflow tract anatomies and highlights the importance of multimodal imaging in procedural planning.