Hostname: page-component-857557d7f7-qdphv Total loading time: 0 Render date: 2025-11-21T18:34:58.155Z Has data issue: false hasContentIssue false
  • English
  • Français

Incidental diagnosis of a complex cyanotic congenital heart defect in a 32-year-old with orbital abscess

Published online by Cambridge University Press:  21 November 2025

Som Singh Open the ORCID record for Som Singh [Opens in a new window] ,
Stephen John ,
Li Xiong  and
Santosh C. Uppu
Som Singh*
Affiliation:
Department of Internal Medicine, University of Texas Health Sciences Center at Houston, Houston, TX, USA
Stephen John
Affiliation:
Department of Internal Medicine, University of Texas Health Sciences Center at Houston, Houston, TX, USA Division of Cardiovascular Disease, Department of Internal Medicine, University of Texas Health Sciences Center at Houston, Houston, TX, USA
Li Xiong
Affiliation:
Children’s Memorial Hermann Hospital, Houston, TX, USA
Santosh C. Uppu
Affiliation:
Department of Internal Medicine, University of Texas Health Sciences Center at Houston, Houston, TX, USA Division of Cardiovascular Disease, Department of Internal Medicine, University of Texas Health Sciences Center at Houston, Houston, TX, USA Adult Congenital Heart Disease Program, University of Texas Health Sciences Center at Houston, Houston, TX, USA
*
Corresponding author: Som Singh; Email: som.p.singh@uth.tmc.edu
Get access Rights & Permissions [Opens in a new window]

Abstract

This case describes a 32-year-old adult male who was incidentally diagnosed with isolated dextrocardia, Double inlet left ventricle (l-looped), l-transposed great arteries with subpulmonary stenosis during evaluation for an orbital abscess. This case highlights protective factors that enabled this patient’s survival into adulthood without cardiac surgeries or medications despite single ventricle physiology, namely his “self-banded” pulmonary flow.

Keywords

dextrocardiacyanotic congenital heart defectorbital abscesshypoxia

Information

Type
Brief Report
Information
Cardiology in the Young , First View , pp. 1 - 5
Check for updates
Copyright
© The Author(s), 2025. Published by Cambridge University Press

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

Article purchase

Temporarily unavailable

References

McLean, K, Downing, T, John, A, Sinha, P, Ito, S. Palliating the unpalliated adult single ventricle patient – options and review of literature. Int J Cardiol Congenit Heart Dis 2023; 13: 100464. DOI: 10.1016/j.ijcchd.2023.100464.Google ScholarPubMed
Opotowsky, AR, Webb, GD. Long-term survival with an unrepaired single ventricle: what is your dangerous idea? Heart Br Card Soc 2016; 102: 172–173. DOI: 10.1136/heartjnl-2015-309063.Google ScholarPubMed
(PDF) Fontan Circulation: How a Model can Hinder or Help to Understand and Manage a Complex Problem. Accessed February 18, 2025. https://www.researchgate.net/publication/388978958_Fontan_Circulation_How_a_Model_can_Hinder_or_Help_to_Understand_and_Manage_a_Complex_Problem.Google Scholar
Poterucha, JT, Anavekar, NS, Egbe, AC, et al. Survival and outcomes of patients with unoperated single ventricle. Heart Br Card Soc 2016; 102: 216–222. DOI: 10.1136/heartjnl-2015-308440.Google ScholarPubMed
Romfh, A, Pluchinotta, FR, Porayette, P, Valente, AM, Sanders, SP. Congenital heart defects in adults : a field guide for cardiologists. J Clin Exp Cardiol 2012; 01: 007. DOI: 10.4172/2155-9880.s8-007.Google Scholar
Franken, LC, Admiraal, M, Verrall, CE, et al. Improved long-term outcomes in double-inlet left ventricle and tricuspid atresia with transposed great arteries: systemic outflow tract obstruction present at birth defines long-term outcome. Eur J Cardiothorac Surg 2017; 51: 1051–1057. DOI: 10.1093/ejcts/ezx022.10.1093/ejcts/ezx022CrossRefGoogle ScholarPubMed
Zheng, WC, d’Udekem, Y, Grigg, LE, et al. Long-term outcomes of patients with single ventricle who do not undergo Fontan palliation. Int J Cardiol Congenit Heart Dis 2023; 12: 100457. DOI: 10.1016/j.ijcchd.2023.100457.Google Scholar
Mazza, GA, Gribaudo, E, Agnoletti, G. The pathophysiology and complications of Fontan circulation. Acta Bio Medica Atenei Parm 2021; 92: e2021260. DOI: 10.23750/abm.v92i5.10893.Google ScholarPubMed
Schleiger, A, Salzmann, M, Kramer, P, et al. Severity of Fontan-associated liver disease correlates with Fontan hemodynamics. Pediatr Cardiol 2020; 41: 736–746. DOI: 10.1007/s00246-020-02291-5.10.1007/s00246-020-02291-5CrossRefGoogle ScholarPubMed
RochéRodríguez, M, DiNardo, JA. The lymphatic system in the fontan patient—Pathophysiology, imaging, and interventions: what the anesthesiologist should know. J Cardiothorac Vasc Anesth 2022; 36: 2669–2678. DOI: 10.1053/j.jvca.2021.07.049.10.1053/j.jvca.2021.07.049CrossRefGoogle ScholarPubMed
Fredenburg, TB, Johnson, TR, Cohen, MD. The Fontan procedure: anatomy, complications, and manifestations of failure. Radiogr Rev Publ Radiol Soc N Am Inc 2011; 31: 453–463. DOI: 10.1148/rg.312105027.Google ScholarPubMed
Fontan-Associated Liver Disease | Circulation. Accessed November 5, 2024. https://www.ahajournals.org/doi/10.1161/CIRCULATIONAHA.120.045597.Google Scholar
Ammash, NM, Warnes, CA. Survival into adulthood of patients with unoperated single ventricle. Am J Cardiol 1996; 77: 542–544. DOI: 10.1016/s0002-9149(97)89356-3.10.1016/S0002-9149(97)89356-3CrossRefGoogle ScholarPubMed
Earing, MG, Cetta, F, Driscoll, DJ, et al. Long-term results of the Fontan operation for double-inlet left ventricle. Am J Cardiol 2005; 96: 291–298. DOI: 10.1016/j.amjcard.2005.03.061.10.1016/j.amjcard.2005.03.061CrossRefGoogle ScholarPubMed
Redefining Expectations of Long-Term Survival After the Fontan Procedure | Circulation. Accessed May 8, 2025. https://www.ahajournals.org/doi/10.1161/circulationaha.113.007764.Google Scholar
Öztürk, AG, Dellborg, M, Damlin, A, Giang, KW, Mandalenakis, Z, Sörensson, P. Long-term survival in patients with univentricular heart: a nationwide, register-based cohort study. Int J Cardiol Congenit Heart Dis 2024; 15: 100503. DOI: 10.1016/j.ijcchd.2024.100503.Google ScholarPubMed
Gómez-Gutiérrez, AK, Morelos-Ulibarri, A, Trejo-Ponce de Leon, D, Gomez-Flores, CD, Luna-Ceron, E. Bacterial brain abscesses in a patient with transposition of the great arteries and interventricular communication. Cureus 2023; 15: e47119. DOI: 10.7759/cureus.47119.Google Scholar
Management of cerebral abscess with large ventricular septal defect in rural area: a case report | Journal of Surgical Case Reports | Oxford Academic. Accessed November 5, 2024. https://academic.oup.com/jscr/article/2023/12/rjad703/7504385.10.1093/jscr/rjad703CrossRefGoogle Scholar
Sangi, R, Ahsan, AK, Shaikh, AS, et al. Incidence, clinical profile and short term outcome of cerebral abscess in cyanotic congenital heart diseases. Heliyon 2023; 9 : e22198. DOI: 10.1016/j.heliyon.2023.e22198.10.1016/j.heliyon.2023.e22198CrossRefGoogle ScholarPubMed