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Are children with protein-losing enteropathy after the Fontan operation at increased risk of cytomegalovirus enteropathy? A report of two cases

Part of: Infectious Functionally Univentricular Heart

Published online by Cambridge University Press:  24 January 2020

Christoph Bauer Open the ORCID record for Christoph Bauer [Opens in a new window]  and
Gerald Tulzer
Christoph Bauer*
Affiliation:
Department for Pediatric Cardiology, Kepler University Hospital GmbH, Johannes Kepler University Linz, Linz, Austria
Gerald Tulzer
Affiliation:
Department for Pediatric Cardiology, Kepler University Hospital GmbH, Johannes Kepler University Linz, Linz, Austria
*
Author for correspondence: C. Bauer, Department for Pediatric Cardiology, Kepler University Hospital GmbH, Johannes Kepler University Linz, 4020Linz, Austria. Tel: 00435768084/28422. E-mail: christoph.bauer@kepleruniklinikum.at
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Abstract

Introduction:

Aetiology of protein-losing enteropathy in single-ventricle type CHD is multi-factorial.

Report:

We describe two Fontan patients with protein-losing enteropathy who presented with cytomegalovirus-associated colitis.

Discussion:

Fontan patients display risk factors for cytomegalovirus-induced gastroenteropathy that may affect lymph angiogenesis, disease development, and progression.

Conclusion:

Cytomegalovirus enteropathy may be common among Fontan patients who suffer from protein-losing enteropathy. Polymerase chain reaction is important for detection.

Keywords

colitiscytomegalovirusendoscopyFontan operationpolymerase chain reactionprotein-losing enteropathy
Type
Brief Report
Information
Cardiology in the Young , Volume 30 , Issue 3 , March 2020 , pp. 431 - 432
Copyright
© Cambridge University Press 2020

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