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An extremely rare clinical entity: congenitally corrected transposition with situs ınversus and single coronary artery presented with complete atrioventricular block in a young man

Part of: Cardiac Morphology

Published online by Cambridge University Press:  12 February 2018

Omer Faruk Cirakoglu Open the ORCID record for Omer Faruk Cirakoglu [Opens in a new window] ,
Ali Bayraktar  and
Muhammet Rasit Sayin
Omer Faruk Cirakoglu*
Affiliation:
Department of Cardiology, Trabzon Ahi Evren Training and Research Hospital, University of Health Science, Trabzon, Turkey
Ali Bayraktar
Affiliation:
Department of Cardiology, Trabzon Ahi Evren Training and Research Hospital, University of Health Science, Trabzon, Turkey
Muhammet Rasit Sayin
Affiliation:
Department of Cardiology, Trabzon Ahi Evren Training and Research Hospital, University of Health Science, Trabzon, Turkey
*
Author for correspondence: O. F. Cirakoglu, MD, Kardiyoloji Anabilim Dali, Ahi Evren Kalp ve Damar Cerrahisi EAH, Saglik Bilimleri Universitesi, Soguksu Vatan St. No: 9, 61040 Trabzon, Turkey. Tel: +90 462 231 04 64; Fax: +90 462 231 04 83; E-mail: omerfcirakoglu@hotmail.com
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Abstract

Congenitally corrected transposition of the great arteries is a rare form of CHD. Situs inversus is a much less common variant of a congenitally corrected transposition of the great arteries. In rare cases, transposition events may be accompanied by various cardiac anomalies. However, situs inversus patients with congenitally corrected transposition, single coronary artery anomaly, and atrioventricular block together have not been reported previously. This combination of abnormalities is presented as a first in the literature.

Keywords

Congenitally corrected transpositionsitus inversussingle coronary anomalyatrioventricular block

Information

Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 5 , May 2018 , pp. 759 - 761
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Copyright
© Cambridge University Press 2018 

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References

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