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A multi-site survey of providers on the management of heart failure with dilated cardiomyopathy in children

Published online by Cambridge University Press:  12 August 2022

Yuk M. Law Open the ORCID record for Yuk M. Law [Opens in a new window] ,
Elizabeth Jacobs-Files ,
Scott Auerbach ,
Ashwin K. Lal ,
Marc Richmond ,
Kurt Schumacher ,
Rakesh Singh  and
Arti Desai
Yuk M. Law*
Affiliation:
Department of Pediatrics, Seattle Children’s Hospital, Seattle, WA, USA
Elizabeth Jacobs-Files
Affiliation:
BJF Research, Seattle, WA, USA
Scott Auerbach
Affiliation:
Department of Pediatrics, Children’s Hospital of Colorado, Aurora, CO, USA
Ashwin K. Lal
Affiliation:
Department of Pediatrics, Primary Children’s Hospital, Salt Lake City, UT, USA
Marc Richmond
Affiliation:
Department of Pediatrics, Morgan Stanley Children’s Hospital, New York, NY, USA
Kurt Schumacher
Affiliation:
Department of Pediatrics, Mott’s Children’s Hospital, Ann Arbor, MI, USA
Rakesh Singh
Affiliation:
Department of Pediatrics, New York University Langone Health, New York, NY, USA
Arti Desai
Affiliation:
Department of Pediatrics, University of Washington School of Medicine, Seattle, WA, USA
*
Author for correspondence: Yuk M. Law, Department of Pediatrics, Seattle Children’s Hospital, 4800 Sand Point Way NE, Seattle, WA 98115, USA. Tel: +1 206 987 4233; Fax: 206-987-3839. E-mail: Yuk.law@seattlechildrens.org
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Abstract

We conducted a scientific survey of paediatric practitioners who manage heart failure with dilated cardiomyopathy in children. The survey covered management from diagnosis to treatment to monitoring, totalling 63 questions. There were 54 respondents from 40 institutions and 3 countries. There were diverse selections of management options by the respondents in general, but also unanimity in some management options. Variation in practice is likely due to the relative paucity of scientific data in this field and lack of strong evidence-based recommendations from guidelines, which presents an opportunity for future research and quality improvement efforts as the evidence base continues to grow.

Keywords

Paediatricschildrenheart failurecardiomyopathysurvey
Type
Original Article
Information
Cardiology in the Young , Volume 33 , Issue 8 , August 2023 , pp. 1296 - 1303
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Copyright
© The Author(s), 2022. Published by Cambridge University Press

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