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Symptomatic Dystonia: Clinical Profile of 46 Brazilian Patients

Published online by Cambridge University Press:  18 September 2015

Henrique B. Ferraz  and
Luiz Augusto F. Andrade
Henrique B. Ferraz*
Affiliation:
Movement Disorders Division, Department of Neurology and Neurosurgery, Escola Paulista de Medicina, São Paulo, Brazil
Luiz Augusto F. Andrade
Affiliation:
Movement Disorders Division, Department of Neurology and Neurosurgery, Escola Paulista de Medicina, São Paulo, Brazil
*
Av. Dr. Altino Arantes, 669 Ap. 43, CEP 04042 Sao Paulo, Brazil
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Abstract:

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Dystonia is a syndrome characterized by sustained muscle contraction, provoking twisting and repeti-tive movements or abnormal postures. It may be classified according to etiology, as idiopathic or symptomatic. We studied 122 Brazilian patients with a dystonic syndrome. Of these, 46 (37.7%) had symptomatic dystonia. The most frequent cause was tardive dystonia (34.8%) followed by perinatal cerebral injury (30.4%). Other causes were stroke (13.0%), encephalitis (6.5%) and Wilson’s disease (4.3%). Cranial trauma, mitochondrial cytopathy and psychogenic, were the least frequent causes with one patient in each category. The etiology in two patients could not be established. Perinatal cerebral injury and postencephalitic dystonia were seen in the younger age group, while post-stroke and tardive dystonia were seen in the older age group.

Type
Articles
Information
Canadian Journal of Neurological Sciences , Volume 19 , Issue 4 , November 1992 , pp. 504 - 507
Copyright
Copyright © Canadian Neurological Sciences Federation 1992

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