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Prenatal diagnosis of double outlet right ventricle with intact ventricular septum in two foetuses

Part of: Functionally Univentricular Heart Cardiac Morphology

Published online by Cambridge University Press:  24 May 2021

Balaganesh Karmegaraj Open the ORCID record for Balaganesh Karmegaraj [Opens in a new window] ,
Balaji Srimurugan  and
Balu Vaidyanathan Open the ORCID record for Balu Vaidyanathan [Opens in a new window]
Balaganesh Karmegaraj*
Affiliation:
Department of Paediatric Cardiology, Amrita Institute of Medical Sciences, Kochi, Kerala, India
Balaji Srimurugan
Affiliation:
Department of Paediatric Cardiology, Amrita Institute of Medical Sciences, Kochi, Kerala, India
Balu Vaidyanathan
Affiliation:
Department of Paediatric Cardiology, Amrita Institute of Medical Sciences, Kochi, Kerala, India
*
Author for correspondence: Dr B. Karmegaraj, MD, DM Assistant Professor, Department of Paediatric Cardiology, Amrita Institute of Medical Sciences, Kochi, Kerala682041, India. Tel: + 91 9746131803; Fax: + 914842802020. E-mail: pedsheartkbg@gmail.com
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Abstract

We describe two cases of an unusual variant of double outlet right ventricle with intact ventricular septum diagnosed prenatally and confirmed by foetal autopsy in a case. The first case had mitral valve atresia, slit-like left ventricle, and normally related great arteries. The second case had mitral valve atresia, hypoplastic left ventricle, parallel outflows with an interrupted aortic arch.

Keywords

Foetusdouble outlet right ventricleintact interventricular septumautopsy
Type
Brief Report
Information
Cardiology in the Young , Volume 31 , Issue 12 , December 2021 , pp. 2041 - 2044
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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