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Ductal stenting for hypoplastic left heart syndrome with right aortic arch associated with 20q11.2 microdeletion syndrome

Published online by Cambridge University Press:  23 September 2025

Yoko Kawai Open the ORCID record for Yoko Kawai [Opens in a new window] ,
Yusuke Kita  and
Shinichiro Oda
Yoko Kawai*
Affiliation:
Department of Pediatrics, Kyoto Prefectural University of Medicine, Kyoto, Japan
Yusuke Kita
Affiliation:
Department of Pediatrics, Kyoto Prefectural University of Medicine, Kyoto, Japan
Shinichiro Oda
Affiliation:
Department of Cardiothoracic Surgery, Kyoto Prefectural University of Medicine, Kyoto, Japan
*
Corresponding author: Yoko Kawai; Email: y-kiwi@koto.kpu-m.ac.jp
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Abstract

Hypoplastic left heart syndrome with a right aortic arch is rare, and performing the Norwood procedure in these cases is challenging. Here, we describe a 3-month-old patient with hypoplastic left heart syndrome having a right aortic arch accompanied by a 20q11.2 microdeletion. Because of cardiac dysfunction, ductal stenting was performed to avoid an early infantile Norwood procedure.

Keywords

Hypoplastic left heart syndromeright aortic archchromosomal anomalyductal stenting

Information

Type
Brief Report
Information
Cardiology in the Young , First View , pp. 1 - 3
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Copyright
© The Author(s), 2025. Published by Cambridge University Press

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References

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